Search on: FACTOR IX 
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Descriptor English:   Factor IX 
Descriptor Spanish:   Factor IX 
Descriptor Portuguese:   Fator IX 
Synonyms English:   Christmas Factor
Plasma Thromboplastin Component
PTC
Autoprothrombin II
Coagulation Factor IX  
Tree Number:   D12.776.124.125.375
D23.119.375
Definition English:   Storage-stable blood coagulation factor acting in the intrinsic pathway. Its activated form, IXa, forms a complex with factor VIII and calcium on platelet factor 3 to activate factor X to Xa. Deficiency of factor IX results in HEMOPHILIA B (Christmas Disease). 
Entry Combination - descr/qualif English:   Factor IX/deficiency use Hemophilia B
 
See Related English:   Coagulants
 
Allowable Qualifiers English:  
AD administration & dosage AE adverse effects
AG agonists AN analysis
AI antagonists & inhibitors BI biosynthesis
CF cerebrospinal fluid CS chemical synthesis
CH chemistry CL classification
CT contraindications DE drug effects
EC economics GE genetics
HI history IM immunology
IP isolation & purification ME metabolism
PK pharmacokinetics PD pharmacology
PH physiology PO poisoning
RE radiation effects SE secretion
ST standards SD supply & distribution
TU therapeutic use TO toxicity
UL ultrastructure UR urine
Record Number:   22169 
Unique Identifier:   D005164 

Occurrence in VHL:
 

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